Diagnosis Code


Code Information

Diagnosis Code: E25.0

Short Description: Congenital adrenogenital disorders assoc w enzyme deficiency

Long Description: Congenital adrenogenital disorders associated with enzyme deficiency

The code E25.0 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E90)
    • Disorders of other endocrine glands (E20-E35)
      • Adrenogenital disorders (E25)
        • E25.0 Congenital adrenogenital disorders assoc w enzyme deficiency

Code Version: 2020 ICD-10-CM


  • 17 alpha-Hydroxyprogesterone aldolase deficiency
  • 3 beta-Hydroxysteroid dehydrogenase deficiency
  • 3-Beta-hydroxy-delta-5-C27-steroid dehydrogenase deficiency
  • Adrenal virilism
  • Adrenal virilism
  • Aldosterone deficiency
  • CAH - desmolase deficiency
  • Cholesterol monooxygenase deficiency
  • Classic congenital adrenal hyperplasia due to 21-hydroxylase deficiency
  • Congenital adrenal hyperplasia
  • Congenital adrenal hyperplasia due to cytochrome P450 oxidoreductase deficiency
  • Congenital adrenal hypoplasia, X-linked
  • Congenital hypoplasia of adrenal gland
  • Congenital lipoid adrenal hyperplasia due to STAR deficiency
  • Corticosterone 18-monooxygenase deficiency
  • Deficiency of 3alpha-hydroxysteroid dehydrogenase
  • Deficiency of 3beta-hydroxysteroid dehydrogenase
  • Deficiency of steroid 11-beta-monooxygenase
  • Deficiency of steroid 21-monooxygenase
  • Disorder of cholesterol catabolism
  • Disorder of cholesterol metabolism
  • Fetal endocrine disorder
  • Fetal virilism
  • Hyperandrogenism due to non-classic 21-hydroxylase deficiency
  • Late onset congenital adrenal hyperplasia
  • Metabolic disorder of fetus
  • Mild steroid 21-hydroxylase deficiency
  • Moderate steroid 21-hydroxylase deficiency
  • Pseudohermaphrodite, female with adrenocortical disorder
  • Salt-losing congenital adrenal hyperplasia
  • Salt-losing congenital adrenal hyperplasia with virilism
  • Severe steroid 21-hydroxylase deficiency
  • Steroid 21-monooxygenase deficiency, salt wasting type
  • Steroid 21-monooxygenase deficiency, simple virilizing type
  • Synthetic defect of bile acids
  • Virilization-adrenogenital syndrome
  • Virilizing syndrome of adrenal origin
  • Virilizing syndrome of adrenal origin

Diagnostic Related Group(s)

The code E25.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v37.0)
  • Endocrine Disorders With Mcc (643)
  • Endocrine Disorders With Cc (644)
  • Endocrine Disorders Without Cc/mcc (645)

References to Index of Diseases and Injuries

The code E25.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Congenital adrenal hyperplasia
    • 21-Hydroxylase deficiency
    • Salt-losing congenital adrenal hyperplasia

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E25.0 Right Arrow 255.2 Adrenogenital disorders
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E25 Adrenogenital disorders
E25.8 Other adrenogenital disorders
E25.9 Adrenogenital disorder, unspecified

This page was last updated on: 10/1/2019