Diagnosis Code

I27.0 PRIMARY PULMONARY HYPERTENSION


Code Information

Diagnosis Code: I27.0

Short Description: Primary pulmonary hypertension

Long Description: Primary pulmonary hypertension

The code I27.0 is VALID for claim submission

Code Classification:

  • Diseases of the circulatory system (I00–I99)
    • Pulmonary heart disease and diseases of pulmonary circulation (I26-I28)
      • Other pulmonary heart diseases (I27)
        • I27.0 Primary pulmonary hypertension

Code Version: 2022 ICD-10-CM


Synonyms

  • Ayerza's syndrome
  • Cor pulmonale
  • Familial primary pulmonary hypertension
  • Heritable pulmonary arterial hypertension
  • Heritable pulmonary arterial hypertension
  • Heritable pulmonary arterial hypertension due to ALK1 or endoglin mutation
  • Heritable pulmonary arterial hypertension due to BMPR2 mutation
  • Idiopathic pulmonary arterial hypertension
  • Idiopathic pulmonary arteriosclerosis
  • Pulmonary arterial pressure increased
  • Right ventricular failure due to pulmonary vascular disease
  • Sporadic primary pulmonary hypertension

Diagnostic Related Group(s)

The code I27.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Other Circulatory System Diagnoses With Mcc (314)
  • Other Circulatory System Diagnoses With Cc (315)
  • Other Circulatory System Diagnoses Without Cc/mcc (316)

References to Index of Diseases and Injuries

The code I27.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Heritable pulmonary arterial hypertension
    • Idiopathic pulmonary arterial hypertension
    • Primary group 1 pulmonary hypertension
    • Primary pulmonary arterial hypertension
  • Type 1 Excludes Notes:
    • persistent pulmonary hypertension of newborn (@P29.30*)
    • pulmonary hypertension NOS (@I27.20*)
    • secondary pulmonary arterial hypertension (@I27.21*)
    • secondary pulmonary hypertension (@I27.29*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
I27.0 Right Arrow 416.0 Prim pulm hypertension

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
I27 Other pulmonary heart diseases
I27.1 Kyphoscoliotic heart disease
I27.2 Other secondary pulmonary hypertension
I27.20 Pulmonary hypertension, unspecified
I27.21 Secondary pulmonary arterial hypertension
I27.22 Pulmonary hypertension due to left heart disease
I27.23 Pulmonary hypertension due to lung diseases and hypoxia
I27.24 Chronic thromboembolic pulmonary hypertension
I27.29 Other secondary pulmonary hypertension
I27.8 Other specified pulmonary heart diseases
I27.81 Cor pulmonale (chronic)
I27.82 Chronic pulmonary embolism
I27.83 Eisenmenger's syndrome
I27.89 Other specified pulmonary heart diseases
I27.9 Pulmonary heart disease, unspecified


This page was last updated on: 10/1/2023