Diagnosis Code

I78.0 HEREDITARY HEMORRHAGIC TELANGIECTASIA


Code Information

Diagnosis Code: I78.0

Short Description: Hereditary hemorrhagic telangiectasia

Long Description: Hereditary hemorrhagic telangiectasia

The code I78.0 is VALID for claim submission

Code Classification:

  • Diseases of the circulatory system (I00–I99)
    • Diseases of arteries, arterioles and capillaries (I70-I79)
      • Diseases of capillaries (I78)
        • I78.0 Hereditary hemorrhagic telangiectasia

Code Version: 2022 ICD-10-CM


Synonyms

  • Brachydactyly of hand
  • Conjunctival telangiectasis
  • Epilepsy telangiectasia syndrome
  • Familial cutaneous telangiectasia and oropharyngeal cancer predisposition syndrome
  • Hereditary benign telangiectasia
  • Hereditary dysplasia of blood vessel
  • Hereditary dysplasia of blood vessel
  • Hereditary dysplasia of blood vessel
  • Hereditary hemorrhagic telangiectasia of gingiva
  • Hypotrichosis, lymphedema, telangiectasia, renal defect syndrome
  • Juvenile polyposis syndrome
  • Juvenile polyposis syndrome with hereditary hemorrhagic telangiectasia
  • Osler hemorrhagic telangiectasia syndrome
  • Osler hemorrhagic telangiectasia syndrome
  • Osler hemorrhagic telangiectasia syndrome
  • Vascular abnormality of conjunctiva

Diagnostic Related Group(s)

The code I78.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Peripheral Vascular Disorders With Mcc (299)
  • Peripheral Vascular Disorders With Cc (300)
  • Peripheral Vascular Disorders Without Cc/mcc (301)

References to Index of Diseases and Injuries

The code I78.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Rendu-Osler-Weber disease

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
I78.0 Right Arrow 448.0 Heredit hemorr telangiec

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
I78 Diseases of capillaries
I78.1 Nevus, non-neoplastic
I78.8 Other diseases of capillaries
I78.9 Disease of capillaries, unspecified


This page was last updated on: 10/1/2023