Diagnosis Code


Code Information

Diagnosis Code: Q80.9

Short Description: Congenital ichthyosis, unspecified

Long Description: Congenital ichthyosis, unspecified

The code Q80.9 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Congenital ichthyosis (Q80)
        • Q80.9 Congenital ichthyosis, unspecified

Code Version: 2020 ICD-10-CM


  • Autosomal dominant mutilating keratoderma
  • Bathing suit ichthyosis
  • CEDNIK syndrome
  • Congenital biliary atresia
  • Congenital cataract ichthyosis syndrome
  • Congenital deformity of foot and ankle
  • Congenital hypotrichia
  • Congenital hypotrichia
  • Congenital ichthyosis of skin
  • Congenital ichthyosis with hypotrichosis syndrome
  • Congenital keratoderma
  • Cutaneous syndrome with ichthyosis
  • Follicular hyperkeratosis
  • Genetic defect of hair shaft
  • Ichthyosis congenita with biliary atresia
  • Ichthyosis, alopecia, eclabion, ectropion, intellectual disability syndrome
  • Ichthyosis, cerebellar degeneration and hepatosplenomegaly
  • Ichthyosis, intellectual disability, dwarfism, renal impairment syndrome
  • Ichthyosis, oral and digital anomalies syndrome
  • Keratoderma hereditarium mutilans with ichthyosis syndrome
  • Keratosis pilaris
  • Keratosis pilaris with ichthyosis and deafness
  • Lamellar ichthyosis
  • Lamellar ichthyosis
  • Limb reduction-ichthyosis syndrome
  • MEDNIK syndrome
  • Multiple sclerosis, ichthyosis, factor VIII deficiency syndrome
  • Mutilating keratoderma
  • Neonatal sclerosing cholangitis, ichthyosis, hypotrichosis syndrome
  • Photosensitivity with ichthyosis, brittle hair, impaired intelligence, decreased fertility and short stature syndrome
  • Premature ovarian failure
  • Sclerosing cholangitis
  • Sclerosing dysplasia of bone, ichthyosis, premature ovarian failure syndrome
  • Severe ichthyoses
  • Trichothiodystrophy
  • X-linked intellectual disability, hypogonadism, ichthyosis, obesity, short stature syndrome
  • XTE syndrome

Diagnostic Related Group(s)

The code Q80.9 is grouped in the following Diagnostic Related Group(s) (MS-DRG v37.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q80.9 Right Arrow 757.1 Ichthyosis congenita

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q80 Congenital ichthyosis
Q80.0 Ichthyosis vulgaris
Q80.1 X-linked ichthyosis
Q80.2 Lamellar ichthyosis
Q80.3 Congenital bullous ichthyosiform erythroderma
Q80.4 Harlequin fetus
Q80.8 Other congenital ichthyosis

This page was last updated on: 10/1/2019