Diagnosis Code

Q81.0 EPIDERMOLYSIS BULLOSA SIMPLEX


Code Information

Diagnosis Code: Q81.0

Short Description: Epidermolysis bullosa simplex

Long Description: Epidermolysis bullosa simplex

The code Q81.0 is VALID for claim submission

Code Classification:

  • Congenital malformations, deformations and chromosomal abnormalities (Q00-Q99)
    • Other congenital malformations (Q80-Q89)
      • Epidermolysis bullosa (Q81)
        • Q81.0 Epidermolysis bullosa simplex

Code Version: 2022 ICD-10-CM


Synonyms

  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal dominant epidermolysis bullosa simplex
  • Autosomal recessive epidermolysis bullosa simplex
  • Autosomal recessive epidermolysis bullosa simplex
  • Autosomal recessive epidermolysis bullosa simplex
  • Basal epidermolysis bullosa simplex
  • Basal epidermolysis bullosa simplex
  • Epidermolysis bullosa simplex
  • Epidermolysis bullosa simplex due to BP230 deficiency
  • Epidermolysis bullosa simplex due to exophilin 5 deficiency
  • Epidermolysis bullosa simplex due to plakophilin deficiency
  • Epidermolysis bullosa simplex herpetiformis
  • Epidermolysis bullosa simplex with circinate migratory erythema
  • Epidermolysis bullosa simplex with hypodontia
  • Epidermolysis bullosa simplex with mottled pigmentation
  • Epidermolysis bullosa simplex with muscular dystrophy
  • Epidermolysis bullosa simplex with pyloric atresia
  • Epidermolysis bullosa simplex, Ogna type
  • Epidermolysis simplex superficialis
  • Gastric atresia
  • Generalized epidermolysis bullosa simplex
  • Intermediate epidermolysis bullosa simplex with cardiomyopathy
  • Keratoderma due to Dowling-Meara type epidermolysis bullosa simplex
  • KRT14 related epidermolysis bullosa simplex
  • Lethal acantholytic erosive disorder
  • Lethal autosomal recessive epidermolysis bullosa simplex
  • Pyloric atresia
  • Suprabasal epidermolysis bullosa simplex

Diagnostic Related Group(s)

The code Q81.0 is grouped in the following Diagnostic Related Group(s) (MS-DRG v39.0)
  • Minor Skin Disorders With Mcc (606)
  • Minor Skin Disorders Without Mcc (607)

References to Index of Diseases and Injuries

The code Q81.0 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Type 1 Excludes Notes:
    • Cockayne's syndrome (@Q87.19*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
Q81.0 Right Arrow 757.39 Skin anomaly NEC

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
Q81 Epidermolysis bullosa
Q81.1 Epidermolysis bullosa letalis
Q81.2 Epidermolysis bullosa dystrophica
Q81.8 Other epidermolysis bullosa
Q81.9 Epidermolysis bullosa, unspecified


This page was last updated on: 10/1/2023