E27.1 PRIMARY ADRENOCORTICAL INSUFFICIENCY

Code Information

  • Diagnosis Code: E27.1
  • Short Description: Primary adrenocortical insufficiency
  • Long Description: Primary adrenocortical insufficiency
  • Code Version: 2025 ICD-10-CM

The code E27.1 is VALID for claim submission

Code Classification

Synonyms

  • Addison's disease
  • Addison's disease due to autoimmunity
  • Adrenocorticotropic hormone resistance syndrome
  • Adrenomyodystrophy
  • Buccal pigmentation due to Addison's disease
  • Congenital hypoplasia of adrenal gland
  • Congenital hypoplasia of adrenal gland
  • Congenital primary adrenocortical hypofunction
  • Endocrine myopathy
  • Familial glucocorticoid deficiency
  • Familial steroid-resistant nephrotic syndrome with adrenal insufficiency
  • Hereditary adrenal unresponsiveness to corticotropin
  • Inherited isolated adrenal insufficiency due to partial CYP11A1 deficiency
  • Melanin pigmentation of oral mucosa
  • Melanosis of mucosa of body orifice
  • Myopathy in Addison's disease
  • Pituitary thyroid hormone resistance
  • Primary adrenocortical insufficiency
  • Primary immunodeficiency with natural killer cell deficiency and adrenal insufficiency
  • Resistance to thyroid hormone syndrome
  • Steroid-resistant nephrotic syndrome

Diagnostic Related Group(s)

The code E27.1 is grouped in the following Diagnostic Related Group(s) MS-DRG V43.0

  1. Endocrine Disorders With Mcc (643)
  2. Endocrine Disorders With Cc (644)
  3. Endocrine Disorders Without Cc/mcc (645)

References to Index of Diseases and Injuries

The code E27.1 has the following ICD-10-CM references to the Index of Diseases and Injuries

  • Inclusion Terms:
    • Addison's disease
    • Autoimmune adrenalitis
  • Type 1 Excludes Notes:
    • Addison only phenotype adrenoleukodystrophy (@E71.528*)
    • amyloidosis (@E85*.-)
    • tuberculous Addison's disease (@A18.7*)
    • Waterhouse-Friderichsen syndrome (@A39.1*)

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E27.1 Right Arrow 255.41 Glucocorticoid deficient
This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E27 Other disorders of adrenal gland
E27.0 Other adrenocortical overactivity
E27.2 Addisonian crisis
E27.3 Drug-induced adrenocortical insufficiency
E27.4 Other and unspecified adrenocortical insufficiency
E27.40 Unspecified adrenocortical insufficiency
E27.49 Other adrenocortical insufficiency
E27.5 Adrenomedullary hyperfunction
E27.8 Other specified disorders of adrenal gland
E27.9 Disorder of adrenal gland, unspecified
This page was last updated on: 10/1/2025
Previous Code
Next Code