Diagnosis Code

E78.1 PURE HYPERGLYCERIDEMIA


Code Information

Diagnosis Code: E78.1

Short Description: Pure hyperglyceridemia

Long Description: Pure hyperglyceridemia

The code E78.1 is VALID for claim submission

Code Classification:

  • Endocrine, nutritional and metabolic diseases (E00–E89)
    • Metabolic disorders (E70-E88)
      • Disorders of lipoprotein metabolism and other lipidemias (E78)
        • E78.1 Pure hyperglyceridemia

Code Version: 2022 ICD-10-CM


Synonyms

  • Endogenous hyperlipidemia
  • Familial hypertriglyceridemia
  • Familial hypertriglyceridemia
  • Fredrickson type IV hyperlipoproteinemia
  • Hyperlipoproteinemia
  • Hypertriglyceridemia
  • Primary genetic hyperlipidemia
  • Primary hypertriglyceridemia
  • Primary hypertriglyceridemia
  • Pure hyperglyceridemia
  • Secondary hypertriglyceridemia
  • Sporadic primary hypertriglyceridemia
  • Transient infantile hypertriglyceridemia and hepatosteatosis
  • Very low density lipoprotinemia
  • Xanthoma due to abnormality of lipid metabolism
  • Xanthoma due to primary hypertriglyceridemia

References to Index of Diseases and Injuries

The code E78.1 has the following ICD-10-CM references to the Index of Diseases and Injuries
  • Inclusion Terms:
    • Elevated fasting triglycerides
    • Endogenous hyperglyceridemia
    • Fredrickson's hyperlipoproteinemia, type IV
    • Hyperlipidemia, group B
    • Hyperprebetalipoproteinemia
    • Very-low-density-lipoprotein-type [VLDL] hyperlipoproteinemia

Crosswalk Information

ICD-10 Code ICD-9 Code ICD-9 Description
E78.1 Right Arrow 272.1 Pure hyperglyceridemia

This ICD-10 to ICD-9 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-10 Code ICD-10 Description
E78 Disorders of lipoprotein metabolism and other lipidemias
E78.0 Pure hypercholesterolemia
E78.00 Pure hypercholesterolemia, unspecified
E78.01 Familial hypercholesterolemia
E78.2 Mixed hyperlipidemia
E78.3 Hyperchylomicronemia
E78.4 Other hyperlipidemia
E78.41 Elevated Lipoprotein(a)
E78.49 Other hyperlipidemia
E78.5 Hyperlipidemia, unspecified
E78.6 Lipoprotein deficiency
E78.7 Disorders of bile acid and cholesterol metabolism
E78.70 Disorder of bile acid and cholesterol metabolism, unspecified
E78.71 Barth syndrome
E78.72 Smith-Lemli-Opitz syndrome
E78.79 Other disorders of bile acid and cholesterol metabolism
E78.8 Other disorders of lipoprotein metabolism
E78.81 Lipoid dermatoarthritis
E78.89 Other lipoprotein metabolism disorders
E78.9 Disorder of lipoprotein metabolism, unspecified


This page was last updated on: 10/1/2023