271.1 GALACTOSEMIA


Code Information

Diagnosis Code: 271.1

Short Description: Galactosemia

Long Description: Galactosemia

Code Classification:

  • Endocrine, nutritional and metabolic diseases, and immunity disorders (240–279)
    • Other metabolic disorders and immunity disorders (270-279)
      • 271 Disorders of carbohydrate transport and metabolism
        • 271.1 Galactosemia

Code Version: 2015 ICD-9-CM


References to Index of Diseases and Injuries

The code 271.1 has the following ICD-9-CM references to the Index of Diseases and Injuries
  • Cataract (anterior cortical) (anterior polar) (black) (capsular) (central) (cortical) (hypermature) (immature) (incipient) (mature)� 366.9
    • associated with
      • galactosemia 271.1 [366.44]
  • Deficiency, deficient
    • galactokinase 271.1
    • galactose-1-phosphate uridyl transferase 271.1
  • Disorder - see also Disease
    • metabolism NEC 277.9
      • galactose-1-phosphate uridyl transferase 271.1
  • Galactosemia (classic) (congenital) 271.1
  • Galactosuria 271.1
  • Jaundice (yellow) 782.4
    • fetus or newborn 774.6
      • due to or associated with
        • galactosemia 271.1 [774.5]
  • Malabsorption 579.9
    • galactose 271.1

Crosswalk Information

The code 271.1 converts into the following ICD-10 code(s):
ICD-9 Code ICD-10 Code ICD-10 Description
271.1 Right Arrow E74.21 Galactosemia
This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code ICD-9 Description
271.0 Glycogenosis
271.2 Hereditary fructose intolerance
271.3 Intestinal disaccharidase deficiencies and disaccharide malabsorption
271.4 Renal glycosuria
271.8 Other specified disorders of carbohydrate transport and metabolism
271.9 Unspecified disorder of carbohydrate transport and metabolism


This page was last updated on: 10/1/2014