747.49 GREAT VEIN ANOMALY NEC

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Code Information

Diagnosis Code: 747.49

Short Description: Great vein anomaly NEC

Long Description: Other anomalies of great veins

Code Classification:

Congenital anomalies (740–759)
- Congenital anomalies (740-759)
  - 747 Other congenital anomalies of circulatory system
    - 747.49 Great vein anomaly NEC

Code Version: 2015 ICD-9-CM

Synonyms

Abnormal connection of hepatic vein to atrium
Abnormal inferior vena caval connection
Abnormality of right superior vena cava
Absence of inferior vena cava
Absence of superior vena cava
Absent right superior vena cava
Alveolar capillary dysplasia with pulmonary venous misalignment
Anatomically corrected malposition with concordant ventriculoarterial connections and parallel great arteries
Anomalous insertion of right superior vena cava to left atrium
Anomalous portal vein termination
Anomalous pulmonary to systemic collateral vein
Anomalous pulmonary venous connection of mixed type
Anomalous pulmonary venous connection of mixed type with one pulmonary venous confluence
Anomalous pulmonary venous connection of mixed type with two pulmonary venous confluences
Atresia of left superior vena cava
Atretic right superior vena cava
Azygos continuation of inferior vena cava to right superior vena cava
Bilateral superior vena cava
Congenital abnormality of great veins and coronary sinus
Congenital absence of inferior vena cava
Congenital absence of portal vein
Congenital absence of superior vena cava
Congenital absence of vena cava
Congenital anomaly of inferior vena cava
Congenital anomaly of superior vena cava
Congenital atresia of inferior vena cava
Congenital atresia of superior vena cava
Congenital coronary sinus stenosis
Congenital dilatation of inferior vena cava
Congenital extrahepatic portal-systemic shunt
Congenital malposition of inferior vena cava
Congenital malposition of superior vena cava
Congenital occlusion of coronary sinus
Congenital partial portal-systemic shunt
Congenital portal-systemic shunt
Congenital pulmonary vein confluence
Congenital pulmonary venous atrium
Congenital splenorenal shunt
Congenital stenosis of inferior vena cava
Congenital stenosis of pulmonary veins
Congenital stenosis of superior vena cava
Congenital stenosis of vena cava
Congenital systemic venous atrium
Congenital transposition of azygos vein
Ductus venosus abnormality
Hepatoportal microvascular dysplasia
Inferior cava to left of spine with right descending aorta
Inferior vena cava anterior and same side as descending aorta
Inferior vena cava connecting to coronary sinus
Inferior vena cava connecting to morphological left atrium
Inferior vena cava interruption with bilateral azygos continuation
Inferior vena cava interruption with left sided hemiazygos continuation
Inferior vena cava interruption with right sided azygos continuation
Inferior vena cava to left of spine
Infracardiac location of anomalous pulmonary venous connection
Infracardiac location of anomalous pulmonary venous connection to hepatic vein
Infracardiac location of anomalous pulmonary venous connection with two descending veins
Interrupted left inferior vena cava
Interrupted right inferior vena cava
Intracardiac location of anomalous pulmonary venous connection
Intracardiac location of anomalous pulmonary venous connection to coronary sinus
Intracardiac location of anomalous pulmonary venous connection to midline with isomeric atria
Intracardiac location of anomalous pulmonary venous connection to right atrium
Left inferior vena cava connecting to left atrium and right atrium
Left inferior vena cava connecting to right sided atrium
Left superior caval vein persisting to coronary sinus
Left superior caval vein persisting to left sided atrium
Left superior vena cava persisting to coronary sinus and then to right sided atrium
Left superior vena cava persisting to right atrium and left atrium
Left superior vena cava persisting to right sided atrium
Obstructed pulmonary venous connection at coronary sinus orifice
Obstructed pulmonary venous connection at interatrial communication
Obstructed pulmonary venous connection due to extrinsic compression
Obstructed pulmonary venous connection due to extrinsic compression at diaphragm
Obstructed pulmonary venous connection due to extrinsic compression between left pulmonary artery and bronchus
Obstructed pulmonary venous connection due to extrinsic compression between right pulmonary artery and trachea
Obstructed pulmonary venous connection due to intrinsic narrowing
Obstructive Eustachian valve
Patent ductus venosus
Persistent common pulmonary vein
Persistent left posterior cardinal vein
Persistent left superior vena cava
Persistent vertical vein
Prominent valve of inferior vena cava
Pulmonary vein atresia
Pulmonary vein stenosis
Pulmonary venous confluence in direct proximity to left atrium
Pulmonary venous confluence in horizontal orientation
Pulmonary venous confluence in vertical orientation
Pulmonary venous confluence remote from left atrium
Pulmonary venous hypertension due to congenital stenosis of pulmonary vein
Pulmonary venous hypoplasia
Right inferior vena cava connecting to left sided atrium
Right superior vena cava connecting to coronary sinus
Right superior vena cava connecting to coronary sinus and then to left sided atrium
Right superior vena cava connecting to left atrium and right atrium
Right superior vena cava persisting to coronary sinus and then to right sided atrium
Saccular dilatation of right superior vena cava
Scimitar syndrome
Scimitar syndrome with additional anomalous pulmonary venous connection
Separate hepatic vein and inferior vena cava connections to heart
Splenoportal vascular anomaly
Subclavian vein stenosis
Supracardiac location of anomalous pulmonary venous connection to hemiazygos vein
Supracardiac location of anomalous pulmonary venous connection to left sided vertical vein
Supracardiac location of anomalous pulmonary venous connection to left superior vena cava
Transposition of pulmonary veins

References to Index of Diseases and Injuries

The code 747.49 has the following ICD-9-CM references to the Index of Diseases and Injuries

Absence (organ or part) (complete or partial)
- pulmonary
  - vein 747.49
- superior vena cava (congenital) 747.49
- vein (congenital) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
  - great 747.49
  - portal 747.49
  - pulmonary 747.49
- vena cava (congenital) (inferior) (superior) 747.49

Agenesis - see also Absence, by site, congenital
- pulmonary
  - vein 747.49
- vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
  - great 747.49
  - portal 747.49
  - pulmonary 747.49
- vena cava (inferior) (superior) 747.49

Anomaly, anomalous (congenital) (unspecified type) 759.9
- opening, pulmonary veins 747.49
- pulmonary 748.60
  - venous
    - connection 747.49
      - partial 747.42
      - total 747.41
    - return 747.49
      - partial 747.42
      - total (TAPVR) (complete) (subdiaphragmatic) (supradiaphragmatic) 747.41
- specified type NEC
  - vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
    - great 747.49
    - portal 747.49
    - pulmonary 747.49
  - vena cava (inferior) (superior) 747.49
- vein(s) (peripheral) NEC (see also Anomaly, peripheral vascular system) 747.60
  - great 747.40
    - specified type NEC 747.49
- venous return (pulmonary) 747.49
  - partial 747.42
  - total 747.41

Atresia, atretic (congenital) 759.89
- pulmonary (artery) 747.31
  - vein 747.49
- vein NEC (see also Atresia, blood vessel) 747.60
  - great 747.49
  - portal 747.49
  - pulmonary 747.49
- vena cava (inferior) (superior) 747.49

Distortion (congenital)
- vein (peripheral) NEC (see also Distortion, peripheral vascular system) 747.60
  - great 747.49
  - portal 747.49
  - pulmonary 747.49
- vena cava (inferior) (superior) 747.49

Hypersplenism 289.4

Hypoplasia, hypoplasis 759.89
- vein(s) (peripheral) NEC (see also Hypoplasia, peripheral vascular system) 747.60
  - great 747.49
  - portal 747.49
  - pulmonary 747.49
- vena cava (inferior) (superior) 747.49

Malposition
- congenital
  - vein(s) (peripheral) NEC (see also Malposition, congenital, peripheral vascular system) 747.60
    - great 747.49
    - portal 747.49
    - pulmonary 747.49
  - vena cava (inferior) (superior) 747.49

Obstruction, obstructed, obstructive
- pulmonary
  - vein, isolated 747.49

Paratyphoid (fever) - see Fever, paratyphoid

Persistence, persistent (congenital) 759.89
- left
  - posterior cardinal vein 747.49
  - superior vena cava 747.49
- sinus
  - venosus with imperfect incorporation in right auricle 747.49

Scimitar syndrome (anomalous venous drainage, right lung to inferior vena cava) 747.49

Stenosis (cicatricial) - see also Stricture
- pulmonary (artery) (congenital) 747.31
  - vein 747.49
    - acquired 417.8
- vena cava (inferior) (superior) 459.2
  - congenital 747.49

Stricture (see also Stenosis) 799.89
- pulmonary, pulmonic
  - vein (congenital) 747.49
    - acquired 417.8
- vena cava (inferior) (superior) NEC 459.2
  - congenital 747.49

Syndrome - see also Disease
- Scimitar (anomalous venous drainage, right lung to inferior vena cava) 747.49

Termination
- anomalous - see also Malposition, congenital
  - portal vein 747.49

Transposition (congenital) - see also Malposition, congenital
- pulmonary veins 747.49

Crosswalk Information

The code 747.49 converts into the following ICD-10 code(s):

ICD-9 Code	ICD-10 Code	ICD-10 Description
747.49	Q26.0	Congenital stenosis of vena cava
	Q26.1	Persistent left superior vena cava
	Q26.8	Other congenital malformations of great veins

This ICD-9 to ICD-10 data is based on the 2018 General Equivalency Mapping (GEM) files published by the Centers for Medicare & Medicaid Services (CMS) for informational purposes only. The data is not an ICD-10 conversion tool and doesn’t guarantee clinical accuracy.

Similar Codes

ICD-9 Code	ICD-9 Description
747.0	Patent ductus arteriosus
747.10	Coarctation of aorta (preductal) (postductal)
747.11	Interruption of aortic arch
747.20	Anomaly of aorta, unspecified
747.21	Anomalies of aortic arch
747.22	Atresia and stenosis of aorta
747.29	Other anomalies of aorta
747.31	Pulmonary artery coarctation and atresia
747.32	Pulmonary arteriovenous malformation
747.39	Other anomalies of pulmonary artery and pulmonary circulation
747.40	Anomaly of great veins, unspecified
747.41	Total anomalous pulmonary venous connection
747.42	Partial anomalous pulmonary venous connection
747.5	Absence or hypoplasia of umbilical artery
747.60	Anomaly of the peripheral vascular system, unspecified site
747.61	Gastrointestinal vessel anomaly
747.62	Renal vessel anomaly
747.63	Upper limb vessel anomaly
747.64	Lower limb vessel anomaly
747.69	Anomalies of other specified sites of peripheral vascular system
747.81	Anomalies of cerebrovascular system
747.82	Spinal vessel anomaly
747.83	Persistent fetal circulation
747.89	Other specified anomalies of circulatory system
747.9	Unspecified anomaly of circulatory system

This page was last updated on: 10/1/2014

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